Surgical treatment of malignant triton tumor of the spinal root (a rare clinical observation)
A. V. Kudziev,
A. S. Nazarov,
Yu. V. Belyakov,
D. A. Sitovskaya,
Yu. M. Zabrodskaya,
E. A. Oleynik,
A. Yu. Orlov https://doi.org/10.56618/2071-2693_2023_15_2_140
Abstract
Malignant newt tumor (MNT) is a highly aggressive malignant neoplasm classified as a variant of malignant peripheral nerve sheath tumor (MPNT) with rhabdomyoblast differentiation. MDRF with divergent (heterologous) differentiation with the presence of a rhabdoid component is extremely rare, accounting for 5 % of all MRRF, which accounts for approximately 2 % of all soft tissue sarcomas. A subgroup of tumors in which malignant Schwann cells coexist with malignant rhabdomyoblasts is called malignant newt tumor (MNT) [10]. In most published clinical observations, newt tumor malignancy occurs in the head, neck, limbs, and trunk [15]. Limited reports of OST are available in the neurooncological literature and are most commonly described as sporadic newt tumor malignancy in the setting of neurofibromatosis type 1 (NF1). A rare clinical case of surgical treatment of OST, Th5 spinal root in a 61-year-old woman is described.
About the Authors
A. V. Kudziev
“National Medical Research Center named after N.N. V. A. Almazova” of the Ministry of Health of Russia
Russian Federation
Russian Federation
St. Petersburg, Akkuratova st. 12
A. S. Nazarov
“National Medical Research Center named after N.N. V. A. Almazova” of the Ministry of Health of Russia
Russian Federation
Russian Federation
St. Petersburg, Akkuratova st. 12
Yu. V. Belyakov
“National Medical Research Center named after N.N. V. A. Almazova” of the Ministry of Health of Russia
Russian Federation
Russian Federation
St. Petersburg, Akkuratova st. 12
D. A. Sitovskaya
“National Medical Research Center named after N.N. V. A. Almazova” of the Ministry of Health of Russia
Russian Federation
Russian Federation
St. Petersburg, Akkuratova st. 12
Yu. M. Zabrodskaya
“National Medical Research Center named after N.N. V. A. Almazova” of the Ministry of Health of Russia
Russian Federation
Russian Federation
St. Petersburg, Akkuratova st. 12
E. A. Oleynik
“National Medical Research Center named after N.N. V. A. Almazova” of the Ministry of Health of Russia
Russian Federation
Russian Federation
St. Petersburg, Akkuratova st. 12
A. Yu. Orlov
“National Medical Research Center named after N.N. V. A. Almazova” of the Ministry of Health of Russia
Russian Federation
Russian Federation
St. Petersburg, Akkuratova st. 12
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Review
For citations:
Kudziev A.V., Nazarov A.S., Belyakov Yu.V., Sitovskaya D.A., Zabrodskaya Yu.M., Oleynik E.A., Orlov A.Yu. Surgical treatment of malignant triton tumor of the spinal root (a rare clinical observation). Russian Neurosurgical Journal named after Professor A. L. Polenov. 2023;15(2):140-144. (In Russ.) https://doi.org/10.56618/2071-2693_2023_15_2_140
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